The guest editors of this Monograph have brought together a compilation of interesting pulmonary manifestations of very different disease entities, such as collagen vascular diseases and vasculitis syndromes. Pulmonary involvement in renal, hepatic, gastrointestinal, neuromuscular, endocrine and metabolic, cardiovascular, immunodeficiency and α1-antitrypsin deficiency diseases is also covered. This book will provide the reader with an interesting overview of the pulmonary involvement in and specific treatment options for different systemic diseases.